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<article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xmlns:ali="http://www.niso.org/schemas/ali/1.0/" article-type="other" dtd-version="1.2" xml:lang="en"><front><journal-meta><journal-id journal-id-type="publisher-id">Head and Neck Tumors</journal-id><journal-title-group><journal-title xml:lang="en">Head and Neck Tumors</journal-title><trans-title-group xml:lang="ru"><trans-title>Опухоли головы и шеи</trans-title></trans-title-group></journal-title-group><issn publication-format="print">2222-1468</issn><issn publication-format="electronic">2411-4634</issn><publisher><publisher-name xml:lang="en">Publishing House ABV Press</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="publisher-id">42</article-id><article-id pub-id-type="doi">10.17650/2222-1468-2013-0-1-56-59</article-id><article-categories><subj-group subj-group-type="toc-heading" xml:lang="en"><subject>CASE REPORTS</subject></subj-group><subj-group subj-group-type="toc-heading" xml:lang="ru"><subject>КЛИНИЧЕСКИЕ СЛУЧАИ</subject></subj-group><subj-group subj-group-type="article-type"><subject></subject></subj-group></article-categories><title-group><article-title xml:lang="en">SKULL BASE LEIOMYOSARCOMA METASTASIS MANIFESTING ITSELF AS OCCIPITAL CONDYLE SYNDROME. A CASE REPORT</article-title><trans-title-group xml:lang="ru"><trans-title>МЕТАСТАЗ ЛЕЙОМИОСАРКОМЫ В ОСНОВАНИЕ ЧЕРЕПА, ПРОЯВИВШИЙСЯ СИНДРОМОМ ЗАТЫЛОЧНОГО МЫЩЕЛКА. ОПИСАНИЕ СЛУЧАЯ</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Stepanyan</surname><given-names>M. A.</given-names></name><name xml:lang="ru"><surname>Степанян</surname><given-names>М. А.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><email>mastepanyan@mail.ru</email><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Cherekaev</surname><given-names>V. A.</given-names></name><name xml:lang="ru"><surname>Черекаев</surname><given-names>В. А.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Kadasheva</surname><given-names>A. B.</given-names></name><name xml:lang="ru"><surname>Кадашева</surname><given-names>А. Б.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Rotin</surname><given-names>D. L.</given-names></name><name xml:lang="ru"><surname>Ротин</surname><given-names>Д. Л.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Vetlova</surname><given-names>E. R.</given-names></name><name xml:lang="ru"><surname>Ветлова</surname><given-names>Е. Р.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib></contrib-group><aff-alternatives id="aff1"><aff><institution xml:lang="en">Acad. N.N. Burdenko Neurosurgery Research Institute, Russian Academy of Medical Sciences, Moscow</institution></aff><aff><institution xml:lang="ru">ФГБУ «НИИ нейрохирургии им. акад. Н.Н. Бурденко» РАМН, Москва</institution></aff></aff-alternatives><pub-date date-type="pub" iso-8601-date="2013-04-15" publication-format="electronic"><day>15</day><month>04</month><year>2013</year></pub-date><volume>3</volume><issue>1</issue><issue-title xml:lang="en"/><issue-title xml:lang="ru"/><fpage>56</fpage><lpage>59</lpage><history><date date-type="received" iso-8601-date="2015-04-16"><day>16</day><month>04</month><year>2015</year></date><date date-type="accepted" iso-8601-date="2015-04-16"><day>16</day><month>04</month><year>2015</year></date></history><permissions><copyright-statement xml:lang="en">Copyright ©; 2013, Stepanyan M.A., Cherekaev V.A., Kadasheva A.B., Rotin D.L., Vetlova E.R.</copyright-statement><copyright-statement xml:lang="ru">Copyright ©; 2013, Степанян М.А., Черекаев В.А., Кадашева А.Б., Ротин Д.Л., Ветлова Е.Р.</copyright-statement><copyright-year>2013</copyright-year><copyright-holder xml:lang="en">Stepanyan M.A., Cherekaev V.A., Kadasheva A.B., Rotin D.L., Vetlova E.R.</copyright-holder><copyright-holder xml:lang="ru">Степанян М.А., Черекаев В.А., Кадашева А.Б., Ротин Д.Л., Ветлова Е.Р.</copyright-holder><ali:free_to_read xmlns:ali="http://www.niso.org/schemas/ali/1.0/"/><license><ali:license_ref xmlns:ali="http://www.niso.org/schemas/ali/1.0/">https://creativecommons.org/licenses/by/4.0</ali:license_ref></license></permissions><self-uri xlink:href="https://ogsh.abvpress.ru/jour/article/view/42">https://ogsh.abvpress.ru/jour/article/view/42</self-uri><abstract xml:lang="en"><p> The occipital condyle syndrome (OCS) is a rare and little-known neurological syndrome pathognomonic of metastatic involvement of the occipital condyle. OCS is the first significant sign of secondary involvement of the atlantooccipital joint in patients with a history of cancer. The early detection of skull base metastases permits timely use of radiation treatments and avoidance of surgical interventions.</p></abstract><trans-abstract xml:lang="ru"><p>Синдром затылочного мыщелка (СЗМ) – редкий и малоизвестный неврологический синдром, патогномоничный для метастатического поражения мыщелка затылочной кости. У больных с онкологическим анамнезом появление СЗМ служит первым достоверным признаком вторичного поражения атланто-окципитального сочленения. Раннее выявление метастазов основания черепа позволяет своевременно применять лучевые методы лечения и избегать хирургических вмешательств.</p></trans-abstract><kwd-group xml:lang="en"><kwd>occipital condyle syndrome</kwd><kwd>metastasis</kwd><kwd>skull base</kwd><kwd>leiomyosarcoma</kwd></kwd-group><kwd-group xml:lang="ru"><kwd>синдром затылочного мыщелка</kwd><kwd>метастаз</kwd><kwd>основание черепа</kwd><kwd>лейомиосаркома</kwd></kwd-group><funding-group/></article-meta></front><body></body><back><ref-list><ref id="B1"><label>1.</label><citation-alternatives><mixed-citation xml:lang="en">1. Greenberg H.S., Deck M.D.F., Vickram B. et al. Metastasis to the base of the skull: clinical findings in 43 patients. Neurology 1981;31:530–7.</mixed-citation><mixed-citation xml:lang="ru">Greenberg H.S., Deck M.D.F., Vickram B. et al. Metastasis to the base of the skull: clinical findings in 43 patients. 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